Respirology case reports
Cystic Lung Changes in Inclusion Body Myositis: An Unusual Pulmonary Manifestation
By Othman G, Ummer T, De Silva H and 2 others.
Abstract
Idiopathic inflammatory myopathies (IIMs) are chronic autoimmune disorders affecting skeletal muscles, with pulmonary involvement in 30%-40% of cases. Inclusion body myositis (IBM) is a distinct subset that usually does not involve the lungs. This report highlights a rare case of inclusion body myositis presenting with pulmonary disease.
Keywords
- cystic lung disease
- idiopathic inflammatory myopathies
- inclusion body myositis



